1 result for "beta-Galactosidase-1/GLB1" in 产品
beta-Galactosidase-1/GLB1 Products
beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates ...
| Reactivity: | Human |
| Source: | CHO |
| Accession #: | AAA51819 |
| Applications: | Enzyme Activity |
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