106 results for "beta-Galactosidase-1/GLB1" in Products

beta-Galactosidase-1/GLB1 Products

beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates ...

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Reactivity: Human
Source: CHO
Accession #: AAA51819
Applications: Enzyme Activity
(3)
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Reactivity: Human, Canine, Monkey
Details: Mouse IgG2A Monoclonal Clone #OTI1C9
Applications: IHC, WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody (OTI1C9) [NBP2-45731]
(16)
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Reactivity: Human, Canine, Monkey
Details: Mouse IgG2A Monoclonal Clone #OTI1C9
Applications: IHC, WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody (OTI1C9)Azide and BSA Free [NBP2-70829]
(15)
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB, Simple Western
Detection of Human  beta -Galactosidase-1/GLB1 antibody by Western Blot.
(2)
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Reactivity: Human
Details: Mouse IgG2A Monoclonal Clone #810226
Applications: WB
Detection of Human  beta -Galactosidase-1/GLB1 antibody by Western Blot.
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Reactivity: Human, Rat
Details: Rabbit IgG Polyclonal
Applications: IHC, WB, ICC/IF
Western Blot: beta-Galactosidase-1/GLB1 Antibody [NBP1-32018]
(2)
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Reactivity: Human
Details: Mouse IgG2a Kappa Monoclonal Clone #6E7
Applications: WB, ELISA, IP
Western Blot: beta-Galactosidase-1/GLB1 Antibody (6E7) [H00002720-M01]
(4)
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Reactivity: Human
Details: Rabbit IgG Polyclonal
Applications: IHC
Immunohistochemistry-Paraffin: beta-Galactosidase-1/GLB1 Antibody [NBP2-49602]
(3)
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Recombinant Monoclonal Antibody

Reactivity: Human, Mouse, Rat
Details: Rabbit IgG Monoclonal Clone #S01-3G1
Applications: WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody (S01-3G1) [NBP3-15007]
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Reactivity: Human
Details: Rabbit IgG Polyclonal
Applications: ICC/IF
Immunocytochemistry/ Immunofluorescence: beta-Galactosidase-1/GLB1 Antibody [NBP2-57793]
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Reactivity: Mouse, Rat
Details: Rabbit IgG Polyclonal
Applications: WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody [NBP3-13394]
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Reactivity: Rat
Sensitivity: 0.10 ng/mL
Assay Range: 0.16 - 10 ng/mL
Applications: ELISA
Rat beta-Galactosidase-1/GLB1 ELISA Kit (Colorimetric)
(2)
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Reactivity: Human
Sensitivity: 1.88 pg/mL
Assay Range: 3.13-200 pg/mL
Applications: ELISA
Human beta-Galactosidase-1/GLB1 ELISA Kit (Colorimetric)
(2)
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Reactivity: Human
Applications: WB
Western Blot: beta-Galactosidase-1/GLB1 Overexpression Lysate [NBL1-11106]
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Reactivity: Human
Source: E. coli
Applications: AC
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Reactivity: Human
Source: E. coli
Applications: AC
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
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Reactivity: Human
Details: Mouse IgG2A Monoclonal Clone #810226
Applications: WB
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