106 results for "beta-Galactosidase-1/GLB1" in Products
beta-Galactosidase-1/GLB1 Products
beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates ...
| Reactivity: | Human |
| Source: | CHO |
| Accession #: | AAA51819 |
| Applications: | Enzyme Activity |
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| Reactivity: | Human, Canine, Monkey |
| Details: | Mouse IgG2A Monoclonal Clone #OTI1C9 |
| Applications: | IHC, WB |
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| Reactivity: | Human, Canine, Monkey |
| Details: | Mouse IgG2A Monoclonal Clone #OTI1C9 |
| Applications: | IHC, WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, Simple Western |
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| Reactivity: | Human |
| Details: | Mouse IgG2A Monoclonal Clone #810226 |
| Applications: | WB |
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| Reactivity: | Human, Rat |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB, ICC/IF |
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| Reactivity: | Human |
| Details: | Mouse IgG2a Kappa Monoclonal Clone #6E7 |
| Applications: | WB, ELISA, IP |
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| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
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Recombinant Monoclonal Antibody
| Reactivity: | Human, Mouse, Rat |
| Details: | Rabbit IgG Monoclonal Clone #S01-3G1 |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | ICC/IF |
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| Reactivity: | Mouse, Rat |
| Details: | Rabbit IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Rat |
| Sensitivity: | 0.10 ng/mL |
| Assay Range: | 0.16 - 10 ng/mL |
| Applications: | ELISA |
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| Reactivity: | Human |
| Sensitivity: | 1.88 pg/mL |
| Assay Range: | 3.13-200 pg/mL |
| Applications: | ELISA |
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| Reactivity: | Human |
| Applications: | WB |
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| Reactivity: | Human |
| Source: | E. coli |
| Applications: | AC |
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| Reactivity: | Human |
| Source: | E. coli |
| Applications: | AC |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Mouse IgG2A Monoclonal Clone #810226 |
| Applications: | WB |
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