3 results for "beta-Galactosidase-1/GLB1" in Products

beta-Galactosidase-1/GLB1 Products

beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates ...

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Reactivity: Human
Details: Sheep IgG Polyclonal
Applications: WB
beta-Galactosidase-1/GLB1 Antibody [CoraFluor™ 1]
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Reactivity: Human
Details: Mouse IgG2A Monoclonal Clone #810226
Applications: WB
beta-Galactosidase-1/GLB1 Antibody (810226) [CoraFluor™ 1]
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Reactivity: Human, Canine, Monkey
Details: Mouse IgG2A Monoclonal Clone #OTI1C9
Applications: IHC, WB
beta-Galactosidase-1/GLB1 Antibody (OTI1C9) [CoraFluor™ 1]
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