204 results for "alpha-Galactosidase A/GLA" in 产品
alpha-Galactosidase A/GLA Products
Galactosidase alpha encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]
| Reactivity: | Human |
| Source: | CHO |
| Accession #: | P06280 |
| Applications: | Enzyme Activity |
| Reactivity: | Human, Mouse |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
| Reactivity: | Human, Rat |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB, IP |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | WB, ICC/IF, IP |
Recombinant Monoclonal Antibody
| Reactivity: | Human, Mouse, Rat |
| Details: | Rabbit IgG Monoclonal Clone #7G8T9 |
| Applications: | WB, ELISA |
Recombinant Monoclonal Antibody
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #30H11 |
| Applications: | IHC, ELISA, Flow |
| Reactivity: | Human |
| Sensitivity: | 46.88 pg/mL |
| Assay Range: | 78.13 - 5000 pg/mL |
| Applications: | ELISA |
| Reactivity: | Human |
| Sensitivity: | 0.49 ng/mL |
| Assay Range: | 0.78 - 50 ng/mL |
| Applications: | ELISA |
| Reactivity: | Monkey |
| Sensitivity: | 46.88 pg/mL |
| Assay Range: | 78.13 - 5000 pg/mL |
| Applications: | ELISA |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human |
| Applications: | WB |
Recombinant Monoclonal Antibody
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #201 |
| Applications: | WB |
| Reactivity: | E. coli |
| Source: | E. coli |
| Applications: | PAGE |
Recombinant Monoclonal Antibody
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #001 |
| Applications: | ELISA, IP |
| Reactivity: | Human |
| Source: | E. coli |
| Applications: | AC |
| Reactivity: | Human |
| Source: | E. coli |
| Applications: | AC |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | ELISA |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, ICC/IF |
Recombinant Monoclonal Antibody
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2520B |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
| Applications: | IHC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, ICC/IF |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, ICC/IF |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, ICC/IF |