24 results for "Lysosomal alpha-Glucosidase" in Products
Lysosomal alpha-Glucosidase Products
GAA encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clin...
| Reactivity: | Human |
| Source: | HEK293 |
| Accession #: | P10253 |
| Applications: | Enzyme Activity |
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Recombinant Monoclonal Antibody.
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2489C |
| Applications: | IHC, WB |
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Recombinant Monoclonal Antibody.
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2489B |
| Applications: | IHC, WB |
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His-tag
| Reactivity: | Mouse |
| Source: | CHO |
| Accession #: | P70699.2 |
| Applications: | Enzyme Activity |
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| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB |
![Immunohistochemistry-Paraffin: LYAG/GAA Antibody [NBP2-38142]](https://beta-resources.rndsystems.com/images/products/LYAG-GAA-Antibody-Immunohistochemistry-Paraffin-NBP2-38142-img0008.jpg "Immunohistochemistry-Paraffin: LYAG/GAA Antibody [NBP2-38142]")
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| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
![LYAG/GAA Antibody - BSA Free Immunohistochemistry-Paraffin: GREB1 Antibody [NBP2-48576]](https://beta-resources.rndsystems.com/images/products/nbp1-93670_rabbit-polyclonal-krt73-antibody-immunohistochemistry-paraffin-2122025156435.jpg "Immunohistochemistry-Paraffin: GREB1 Antibody [NBP2-48576]")
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| Reactivity: | Mouse |
| Applications: |
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| Reactivity: | Human |
| Applications: |
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| Reactivity: | Human |
| Details: | Mouse IgG1 kappa Monoclonal Clone #3C6 |
| Applications: | WB, ELISA |
![Western Blot: LYAG/GAA Antibody (3C6) [H00002548-M01]](https://beta-resources.rndsystems.com/images/products/LYAG-GAA-Antibody-3C6-Western-Blot-H00002548-M01-img0001.jpg "Western Blot: LYAG/GAA Antibody (3C6) [H00002548-M01]")
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| Reactivity: | Cynomolgus Monkey |
| Applications: |
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Recombinant monoclonal antibody expressed in HEK293F cells
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #5E5 |
| Applications: | IHC, ELISA |
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Recombinant Monoclonal Antibody
| Reactivity: | Human, Mouse, Rat |
| Details: | Rabbit IgG Monoclonal Clone #SR1086 |
| Applications: | WB |
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| Reactivity: | Human |
| Details: | Mouse IgG Polyclonal |
| Applications: | WB |
![Western Blot: LYAG/GAA Antibody [H00002548-B01P]](https://beta-resources.rndsystems.com/images/products/LYAG-GAA-Antibody-Western-Blot-H00002548-B01P-img0002.jpg "Western Blot: LYAG/GAA Antibody [H00002548-B01P]")
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| Reactivity: | E. coli |
| Applications: | Func |
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| Reactivity: | Mouse |
| Sensitivity: | 18.75 pg/mL |
| Assay Range: | 31.25 - 2000 pg/mL |
| Applications: | ELISA |
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| Reactivity: | Rat |
| Sensitivity: | 0.94 ng/mL |
| Assay Range: | 1.56 - 100 ng/mL |
| Applications: | ELISA |
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| Reactivity: | Human |
| Sensitivity: | 0.09 ng/mL |
| Assay Range: | 0.16 - 10 ng/mL |
| Applications: | ELISA |
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| Reactivity: | Human |
| Applications: | WB |
![Western Blot: LYAG/GAA Overexpression Lysate [NBL1-10901]](https://beta-resources.rndsystems.com/images/products/GAA-Overexpression-Lysate-Adult-Normal-Western-Blot-NBL1-10901-img0002.jpg "Western Blot: LYAG/GAA Overexpression Lysate [NBL1-10901]")
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| Reactivity: | Human |
| Applications: | WB |
![Western Blot: LYAG/GAA Overexpression Lysate [NBL1-10902]](https://beta-resources.rndsystems.com/images/products/GAA-Overexpression-Lysate-Adult-Normal-Western-Blot-NBL1-10902-img0001.jpg "Western Blot: LYAG/GAA Overexpression Lysate [NBL1-10902]")
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| Reactivity: | Human |
| Applications: | WB |
![Western Blot: LYAG/GAA Overexpression Lysate [NBP2-09270]](https://beta-resources.rndsystems.com/images/products/GAA-Overexpression-Lysate-Adult-Normal-Western-Blot-NBP2-09270-img0001.jpg "Western Blot: LYAG/GAA Overexpression Lysate [NBP2-09270]")
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Recombinant Monoclonal Antibody
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #5L2L10 |
| Applications: | WB, ELISA |
![Western Blot: LYAG/GAA Antibody (5L2L10) [NBP3-15698]](https://beta-resources.rndsystems.com/images/products/LYAG-GAA-Antibody-5L2L10-Western-Blot-NBP3-15698-img0001.jpg "Western Blot: LYAG/GAA Antibody (5L2L10) [NBP3-15698]")
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| Reactivity: | Human |
| Source: | E. coli |
| Applications: | AC |
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| Reactivity: | Human |
| Source: | E. coli |
| Applications: | AC |
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| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB, ICC/IF |
![Immunocytochemistry/ Immunofluorescence: LYAG/GAA Antibody [NBP1-69295]](https://beta-resources.rndsystems.com/images/products/LYAG-GAA-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-69295-img0003.jpg "Immunocytochemistry/ Immunofluorescence: LYAG/GAA Antibody [NBP1-69295]")
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