42 results for "Dysferlin" in Products

Dysferlin Products

Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM.

Reactivity: Human
Details: Rabbit IgG Polyclonal
Applications: IHC, ICC/IF
Immunocytochemistry/ Immunofluorescence: Dysferlin Antibody [NBP1-84696]
(7)
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Recombinant Monoclonal Antibody

Reactivity: Human, Mouse
Details: Rabbit IgG Monoclonal Clone #JF05-54
Applications: IHC, WB, ICC/IF
Western Blot: Dysferlin Antibody (JF05-54) [NBP2-66814]
(7)
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Recombinant Monoclonal Antibody

Reactivity: Human
Details: Rabbit IgG Monoclonal Clone #3U1P9
Applications: IHC, WB, ELISA
Western Blot: Dysferlin Antibody (3U1P9) [NBP3-15781]
(11)
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Immunohistochemistry-Paraffin: Dysferlin Antibody (CL10888) [NBP3-07994]
(6)
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Reactivity: Human
Details: Rabbit IgG Polyclonal
Applications: IHC
Immunohistochemistry-Paraffin: Dysferlin Antibody [NBP1-84695]
(6)
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Dysferlin Antibody (CL10888) - Azide and BSA Free Immunohistochemistry-Paraffin: Dysferlin Antibody [NBP3-43895]
(6)
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Recombinant Monoclonal Antibody

Reactivity: Human, Mouse
Details: Rabbit IgG Monoclonal Clone #SR2944
Applications: IHC, WB, ICC/IF
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Reactivity: Human, Mouse
Details: Rabbit IgG Monoclonal Clone #24GB3235
Applications: WB, Flow, ICC/IF
Novus Antibodies
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Reactivity: Human
Sensitivity: 0.141 ng/mL (example only; lot dependent)
Assay Range: 0.312 - 20 ng/mL (example only; lot dependent)
Applications: ELISA
Human Dysferlin ELISA Kit (Colorimetric)
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Reactivity: Human
Sensitivity: 0.141 ng/mL (example only; lot dependent)
Assay Range: 0.312 - 20 ng/mL (example only; lot dependent)
Applications: ELISA
Human Dysferlin - Ready-To-Use ELISA Kit (Colorimetric)
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Reactivity: Human
Source: E. coli
Applications: AC
Dysferlin Recombinant Protein Antigen
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Reactivity: Human
Source: E. coli
Applications: AC
Dysferlin Recombinant Protein Antigen
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Dysferlin Antibody (CL10888) [CoraFluor™ 1]
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #CL10888
Applications: IHC, WB
Novus Antibodies
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