80 results for "Glucosylceramidase/GBA" in Products

Glucosylceramidase/GBA Products

Glucosylceramidase is a lysosomal enzyme that cleaves the beta-glucosidic linkage of glucosylceramide, an intermediate in glycolipid metabolism. The mature enzyme has 497 amino acids with a molecular weight of 62 kDa. Glycosylation occurs at four of five N-glycosylation sites and is essential for the trafficking and activity of the enzyme. The enzyme is activated in lysosomes by saposin C, although the mechanism of activation is not well understood. Defects in Glucosylceramidase are the cause ...

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Reactivity: Human
Source: CHO
Accession #: P04062.3
Applications: Enzyme Activity
(3)
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Reactivity: Human, Plant
Details: Mouse IgG2a Kappa Monoclonal Clone #2E2
Applications: IHC, WB, ELISA, ICC/IF, IP
Western Blot: Glucosylceramidase/GBA Antibody (2E2) [H00002629-M01]
(6)
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Recombinant Monoclonal Antibody

Reactivity: Human, Mouse, Rat
Details: Rabbit IgG Monoclonal Clone #JM10-76
Applications: KO, IHC, WB, Flow, ICC/IF
Glucosylceramidase/GBA Antibody (JM10-76) Western Blot Shows Glucosylceramidase/GBA Specificity Using Knockout Cell Line.
(10)
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Reactivity: Human, Mouse, Zebrafish
Details: Rabbit IgG Polyclonal
Applications: IHC, WB, ICC/IF
Immunohistochemistry-Paraffin: Glucosylceramidase/GBA Antibody [NBP1-32271]
(6)
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Recombinant Monoclonal Antibody

Reactivity: Human, Rat
Details: Rabbit IgG Monoclonal Clone #8O3Z7
Applications: IHC, WB
Western Blot: Glucosylceramidase/GBA Antibody (8O3Z7) [NBP3-15637]
(10)
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Reactivity: Human, Mouse, Rat
Details: Mouse IgG2A Monoclonal Clone #OTI4G4
Applications: IHC, WB
Western Blot: Glucosylceramidase/GBA Antibody (OTI4G4) [NBP2-45829]
(5)
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Reactivity: Human, Mouse, Rat
Details: Mouse IgG2A Monoclonal Clone #OTI4G4
Applications: IHC, WB
Western Blot: Glucosylceramidase/GBA Antibody (OTI4G4)Azide and BSA Free [NBP2-70803]
(5)
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Reactivity: Human
Details: Mouse IgG Polyclonal
Applications: WB
Western Blot: Glucosylceramidase/GBA Antibody [H00002629-B01P]
(2)
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Irreversible glucocerebrosidase (β-glucosidase) inhibitor; used to generate Gaucher disease models

Chemical Name: DL-1,2-Anhydro-myo-inositol
Irreversible glucocerebrosidase (β-glucosidase) inhibitor; used to generate Gaucher disease models
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Reactivity: Non-species specific
Applications: Enzyme Activity, Func
Enzyme Activity: Glucosylceramidase/GBA Assay Kit (Colorimetric) [KA1611]
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Reactivity: Human
Applications:
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Reactivity: Human
Applications: WB
Western Blot: Glucosylceramidase/GBA Overexpression Lysate [NBL1-10989]
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Reactivity: Human
Applications: WB
Western Blot: Glucosylceramidase/GBA Overexpression Lysate [NBL1-10990]
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Reactivity: Human
Applications: WB
Western Blot: Glucosylceramidase/GBA Overexpression Lysate [NBP2-08846]
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Reactivity: Human
Applications: WB
Western Blot: Glucosylceramidase/GBA Overexpression Lysate [NBP2-09097]
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Recombinant Monoclonal Antibody

Reactivity: Human
Details: Rabbit IgG Monoclonal Clone #4H4
Applications: WB, ELISA
Glucosylceramidase/GBA Antibody (4H4)
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