80 results for "Glucosylceramidase/GBA" in Products
Glucosylceramidase/GBA Products
Glucosylceramidase is a lysosomal enzyme that cleaves the beta-glucosidic linkage of glucosylceramide, an intermediate in glycolipid metabolism. The mature enzyme has 497 amino acids with a molecular weight of 62 kDa. Glycosylation occurs at four of five N-glycosylation sites and is essential for the trafficking and activity of the enzyme. The enzyme is activated in lysosomes by saposin C, although the mechanism of activation is not well understood. Defects in Glucosylceramidase are the cause ...
| Reactivity: | Human |
| Source: | CHO |
| Accession #: | P04062.3 |
| Applications: | Enzyme Activity |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF, Simple Western |
| Reactivity: | Human, Plant |
| Details: | Mouse IgG2a Kappa Monoclonal Clone #2E2 |
| Applications: | IHC, WB, ELISA, ICC/IF, IP |
Recombinant Monoclonal Antibody
| Reactivity: | Human, Mouse, Rat |
| Details: | Rabbit IgG Monoclonal Clone #JM10-76 |
| Applications: | KO, IHC, WB, Flow, ICC/IF |
| Reactivity: | Human, Mouse, Zebrafish |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB, ICC/IF |
Recombinant Monoclonal Antibody
| Reactivity: | Human, Rat |
| Details: | Rabbit IgG Monoclonal Clone #8O3Z7 |
| Applications: | IHC, WB |
| Reactivity: | Human, Mouse, Rat |
| Details: | Mouse IgG2A Monoclonal Clone #OTI4G4 |
| Applications: | IHC, WB |
| Reactivity: | Human, Mouse, Rat |
| Details: | Mouse IgG2A Monoclonal Clone #OTI4G4 |
| Applications: | IHC, WB |
| Reactivity: | Human |
| Details: | Mouse IgG Polyclonal |
| Applications: | WB |
Irreversible glucocerebrosidase (β-glucosidase) inhibitor; used to generate Gaucher disease models
| Chemical Name: | DL-1,2-Anhydro-myo-inositol |
| Reactivity: | Non-species specific |
| Applications: | Enzyme Activity, Func |
| Reactivity: | Human |
| Applications: |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #812201 |
| Applications: | KO, WB, ICC/IF |
| Reactivity: | Human |
| Applications: | WB |
| Reactivity: | Human |
| Applications: | WB |
| Reactivity: | Human |
| Applications: | WB |
| Reactivity: | Human |
| Applications: | WB |
Recombinant Monoclonal Antibody
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #4H4 |
| Applications: | WB, ELISA |