86 results for "Lysosomal alpha-Glucosidase" in Products

Lysosomal alpha-Glucosidase Products

GAA encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq]

Reactivity: Human
Source: HEK293
Accession #: P10253
Applications: Enzyme Activity
(3)
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Reactivity: Human
Details: Rabbit IgG Polyclonal
Applications: IHC, WB
Immunohistochemistry-Paraffin: LYAG/GAA Antibody [NBP2-38142]
(6)
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His-tag

Reactivity: Mouse
Source: CHO
Accession #: P70699.2
Applications: Enzyme Activity
(2)
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Reactivity: Human
Details: Rabbit IgG Polyclonal
Applications: IHC
LYAG/GAA Antibody - BSA Free Immunohistochemistry-Paraffin: GREB1 Antibody [NBP2-48576]
(5)
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α-glucosidase I and II inhibitor; also inhibits ceramide-specific glycosyltransferases and exhibits broad spectrum antiviral activity

Alternate Names: N-Butyldeoxynojirimycin hydrochloride,NB-DNJ
Chemical Name: (2R,3R,4R,5S)-1-Butyl-2-(hydroxymethyl)-3,4,5-piperidinetriol hydrochloride
α-glucosidase I and II inhibitor; also inhibits ceramide-specific glycosyltransferases and exhibits broad spectrum antiviral activity
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Reactivity: Mouse
Applications:
R&D Systems VersaClone cDNA Plasmids
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Reactivity: Human
Applications:
R&D Systems VersaClone cDNA Plasmids
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Reactivity: Human
Details: Mouse IgG1 kappa Monoclonal Clone #3C6
Applications: WB, ELISA
Western Blot: LYAG/GAA Antibody (3C6) [H00002548-M01]
(2)
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Reactivity: Cynomolgus Monkey
Applications:
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